CARDIAC MUSCLE DISEASE
Non-Compaction Cardiomyopathy
Non-Compaction Cardiomyopathy (NCCM) is a genetic heart muscle disease in which coarser muscle fibre bundles and cavities are caused in the heart muscle wall. This change can reduce the heart’s pumping power. NCCM can develop spontaneously, but can also have a hereditary cause if the predisposition runs in a family.
The disease NCCM is also called LVNC (Left Ventricular Non-Compaction Cardiomyopathy), where the left ventricle is affected.
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Possible signs and symptoms of NCCM are:
Shortness of breath, problems by exercise and reduced endurance
Heart palpitations and chest pain
Cardiac arrhythmia: severe arrhythmia can sometimes cause dizziness, fainting and even sudden cardiac death
In the course of life
The changes of the heart muscle can develop slowly over the course of life, usually in adulthood but sometimes from the age of 10 years. The symptoms vary from gene carrier to gene carrier: some may experience severe heart problems (and eventually heart failure) while others have no symptoms at all. In case of symptoms, it is important to discuss it with your GP so that an additional cardiovascular examination can be carried out.
ACCORDING TO SIGNS AND SYMPTOMS
Possible treatments
Medication
Depending on symptoms, adequate medication can be prescribed.
ICD / Pacemaker
If there is a risk of dangerous cardiac arrhythmia, an ICD can be implemented.
Heart surgery
In some severe cases, a VAD and/or heart transplant can be necessary.
Lifestyle
NCCM patients should strongly avoid intensive exercise and stress.
Cardiovascular examination
Echo
An ultrasound of the heart provides a clear image and sound of the function and shape of the heart muscle and valves.
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MRI Scan
The MRI examination, which generates radio wave (magnetic) signals, provides a clear picture of the heart (chambers).
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ECG
In an electrocardiogram, the electrical signals of the heartbeats are properly recorded and can be analyzed.
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• Cardiovascular examination may also include a Holter monitor test and/or an exercise test/cycle test.
Discuss it with your GP or cardiologist
If you’re experiencing some signs and symptoms, or if other family members have been found with a predisposition for the genetic heart disease NCCM, please discuss it with your GP/cardiologist so that additional cardiovascular examination can be assessed.
